Heptadecanoyl-L-carnitine-d3 HCl (N-methyl-d3)
- CAS NO.:173686-69-6
- Empirical Formula: C24H48ClNO4
- Molecular Weight: 450.1
- Update Date: 2025-04-17 18:22:24
What is Heptadecanoyl-L-carnitine-d3 HCl (N-methyl-d3)?
Biological Activity
Heptadecanoyl-L-carnitine is a long-chain acylcarnitine composed of heptadecanoic acid and L-carnitine . Levels of heptadecanoyl-L-carnitine are increased in dried blood spots from neonates with propionic or methylmalonic acidemias, inborn errors of metabolism characterized by a deficiency in the activity of propionyl-CoA carboxylase or L-methylmalonyl-CoA mutase or its cofactor 5-deoxyadenosylcobalamin, respectively.1
References
1.Malvagia, S., Haynes, C.A., Grisotto, L., et al.Heptadecanoylcarnitine (C17) a novel candidate biomarker for propionic and methylmalonic acidemias during expanded newborn screeningClin. Chim. Acta450342-348(2015)
Properties of Heptadecanoyl-L-carnitine-d3 HCl (N-methyl-d3)
| storage temp. | -20°C |
| solubility | Chloroform: 30 mg/ml,Methanol: 30 mg/ml |
| form | A crystalline solid |
Safety information for Heptadecanoyl-L-carnitine-d3 HCl (N-methyl-d3)
Computed Descriptors for Heptadecanoyl-L-carnitine-d3 HCl (N-methyl-d3)
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